EPENDIMOMA WITH EXTRACEREBRAL INTRAORBITAL RELAPSE: CASE REPORT

Abstract

Ependymomas are rare neuroepithelial tumors originating from a type of glial cell, called the ependymal cell. In general they correspond to about 1.2-7.8% of all intracranial neoplasms and 2-6% of all gliomas. Although ependymoma accounts for only 2-3% of all primary brain tumors, ependymoma is the fourth most common cerebral neoplasm in children, especially children younger than 3 years. In patients less than 20 years of age, the majority (90%) of ependymomas are infratentorial, more precisely, from the IV ventricle. Despite this, in adults, medullary ependymomas are more frequent (60%). In this context, supratentorial and extraventricular ependymomas, as in the case reported, are infrequent in both adults and children. Both sexes are equally affected. unusual recurrence of intracranial ependymomas occurs in almost 50% of the cases, and the result of its follow-up is not very favorable. In another perspective, extracerebral recurrence of ependymomas is extremely rare, being even more unusual intraorbital site of the case in question.